Localization of nervonic acid beta-oxidation in human and rodent peroxisomes: impaired oxidation in Zellweger syndrome and X-linked adrenoleukodystrophy.
第一作者:
R,Sandhir
第一单位:
Division of Developmental Neurogenetics, Department of Pediatrics, Medical University of South Carolina, Charleston, SC 29425, USA.
作者:
医学主题词
肾上腺脑白质营养不良(Adrenoleukodystrophy);动物(Animals);细胞系(Cell Line);辅酶A连接酶类(Coenzyme A Ligases);脂肪酸类(Fatty Acids);脂肪酸类, 单不饱和(Fatty Acids, Monounsaturated);成纤维细胞(Fibroblasts);基因连锁(Genetic Linkage);人类(Humans);微体(Microbodies);神经胶质(Neuroglia);氧化还原(Oxidation-Reduction);大鼠(Rats);大鼠, Sprague-Dawley(Rats, Sprague-Dawley);阻遏蛋白质类(Repressor Proteins);酿酒酵母蛋白质类(Saccharomyces cerevisiae Proteins);X染色体(X Chromosome);Zellweger综合征(Zellweger Syndrome)
PMID
9799802
发布时间
2025-01-03
- 浏览46
Journal of lipid research
2161-71页
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