摘要卡梅现象也称卡梅综合征,是发生于卡波西样血管内皮瘤或丛状血管瘤,并以严重血小板减少和消耗性凝血功能障碍为特征的临床综合征.该病较为罕见,多发于婴幼儿,病情凶险,得不到及时治疗者,可危及生命.该文对卡梅现象的临床表现、发病机制、诊断及治疗等方面的研究进展进行综述.
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abstractsKasabach-Merritt phenomenon (KMP),also known as Kasabach-Merritt syndrome,is a rare syndrome associated with Kaposiform haemangioendothelioma or tufted angioma,and characterized by thrombocytopenia and consumptive coagulopathy.KMP onsets early and progresses quickly.If diagnosis and treatment delayed,it can be life-threatening.In this paper,the progress of clinical manifestations,pathogenesis,diagnosis and treatment of KMP are summarized.
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