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Modulation of oxidative phosphorylation and redox homeostasis in mitochondrial NDUFS4 deficiency via mesenchymal stem cells.

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第一作者: Marlen,Melcher
第一单位: Department of General Pediatrics, Neonatology and Pediatric Cardiology, University Children's Hospital, Heinrich Heine University Düsseldorf, Moorenstraße 5, 40225, Düsseldorf, Germany.
作者单位: Department of General Pediatrics, Neonatology and Pediatric Cardiology, University Children's Hospital, Heinrich Heine University Düsseldorf, Moorenstraße 5, 40225, Düsseldorf, Germany. [1] Division of Pediatric Stem Cell Therapy, Clinic for Pediatric Oncology, Hematology and Clinical Immunology, Medical Faculty, Heinrich Heine University Medical Center, Düsseldorf, Germany. [2] Institute of Biochemistry and Molecular Biology I, Medical Faculty, Heinrich Heine University, Düsseldorf, Germany. [3] Department of Biochemistry (286), Radboud Institute for Molecular Life Sciences, Radboud University Nijmegen (Radboudumc), Nijmegen, The Netherlands. [4] Radboud Center for Mitochondrial Medicine (RCMM), Department of Pediatrics, 774 Translational Metabolic Laboratory (TML), Radboud University Medical Center, P.O. Box 9101, 6500 HB, Nijmegen, The Netherlands. [5] Department of General Pediatrics, Neonatology and Pediatric Cardiology, University Children's Hospital, Heinrich Heine University Düsseldorf, Moorenstraße 5, 40225, Düsseldorf, Germany. Felix.Distelmaier@med.uni-duesseldorf.de. [6]
DOI 10.1186/s13287-017-0601-7
PMID 28646906
发布时间 2019-12-10
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Stem cell research & therapy

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