摘要INTRODUCTIONIdiopathic pulmonary fibrosis (IPF) is a specific type of chronic progressive fibrosing interstitial pneumonia associated with a histopathologic pattern of usual interstitial pneumonia.IPF is typically considered to be a lung-limited disorder.Although the primary manifestations of IPF are pulmonary in nature,IPF is increasingly recognized as a systemic disease due to its strong association with comorbidities and complications.
作者单位Department of Respiratory Medicine, The Second Xiangya Hospital, Central South University, Changsha, Hunan 410011, China[1]Department of Respiratory Medicine, The Second Xiangya Hospital, Central South University, Changsha, Hunan 410011, China;Research Unit of Respiratory Disease, Central South University, Changsha, Hunan 410011, China;Diagnosis and Treatment Central of Respiratory Disease, Central South University, Changsha, Hunan 410011, China[2]
The study was supported by grants from the National Natural Science Foundation of Chinathe Natural Science Foundation of Hunan Provincethe National Key Clinical Specialty Construction Projects