The muscle chloride channel ClC-1 has a double-barreled appearance that is differentially affected in dominant and recessive myotonia.
第一作者:
C,Saviane
第一单位:
Istituto di Cibernetica e Biofisica, CNR, I-16149 Genova, Italy.
作者:
医学主题词
算法(Algorithms);动物(Animals);氯化物通道(Chloride Channels);电生理学(Electrophysiology);基因, 显性(Genes, Dominant);基因, 隐性(Genes, Recessive);人类(Humans);氢离子浓度(Hydrogen-Ion Concentration);离子通道闸门(Ion Channel Gating);动力学(Kinetics);膜电位(Membrane Potentials);肌蛋白质类(Muscle Proteins);肌, 骨骼(Muscle, Skeletal);肌强直(Myotonia);卵母细胞(Oocytes);膜片钳术(Patch-Clamp Techniques);光滑爪蟾(Xenopus laevis)
DOI
10.1085/jgp.113.3.457
PMID
10051520
发布时间
2025-05-29
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