Sustained correction of B-cell development and function in a murine model of X-linked agammaglobulinemia (XLA) using retroviral-mediated gene transfer.
第一作者:
Phyllis W,Yu
第一单位:
Children's Hospital and Regional Medical Center, 307 Westlake Ave North, Suite 300, Seattle, WA 98109, USA.
作者:
主题词
丙种球蛋白缺乏血症(Agammaglobulinemia);动物(Animals);B-淋巴细胞(B-Lymphocytes);骨髓移植(Bone Marrow Transplantation);细胞分裂(Cell Division);细胞谱系(Cell Lineage);染色体, 人, X(Chromosomes, Human, X);疾病模型, 动物(Disease Models, Animal);基因表达(Gene Expression);基因转移技术(Gene Transfer Techniques);造血干细胞(Hematopoietic Stem Cells);人类(Humans);小鼠(Mice);小鼠, 近交C57BL(Mice, Inbred C57BL);小鼠, 突变型(Mice, Mutant Strains);蛋白酪氨酸激酶类(Protein-Tyrosine Kinases);逆转录病毒科(Retroviridae)
DOI
10.1182/blood-2003-09-3044
PMID
15142874
发布时间
2022-01-29
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Blood
1281-90页
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