A non-BRICHOS surfactant protein c mutation disrupts epithelial cell function and intercellular signaling.
第一作者:
Markus,Woischnik
第一单位:
Department of Pneumology, Dr von Hauner Children's Hospital, Ludwig-Maximilians University, Lindwurmstr 4, Munich 80337, Germany.
作者:
医学主题词
氨基酸取代(Amino Acid Substitution);动物(Animals);硫唑嘌呤(Azathioprine);支气管肺泡灌洗液(Bronchoalveolar Lavage Fluid);CD4阳性T淋巴细胞(CD4-Positive T-Lymphocytes);钙联蛋白(Calnexin);钙网蛋白(Calreticulin);细胞系(Cell Line);环磷酰胺(Cyclophosphamide);上皮细胞(Epithelial Cells);HSP70热休克蛋白质类(HSP70 Heat-Shock Proteins);HSP90热休克蛋白质类(HSP90 Heat-Shock Proteins);人类(Humans);羟氯喹(Hydroxychloroquine);肺疾病, 间质性(Lung Diseases, Interstitial);甲泼尼龙(Methylprednisolone);小鼠(Mice);突变(Mutation);磷脂酰胆碱类(Phosphatidylcholines);肺表面活性物质相关蛋白质C(Pulmonary Surfactant-Associated Protein C);受体, CCR2(Receptors, CCR2);受体, 白细胞介素8A(Receptors, Interleukin-8A);信号传导(Signal Transduction)
DOI
10.1186/1471-2121-11-88
PMID
21092132
发布时间
2021-10-20
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