Drosophila carrying pex3 or pex16 mutations are models of Zellweger syndrome that reflect its symptoms associated with the absence of peroxisomes.
第一作者:
Minoru,Nakayama
第一单位:
Genome and Drug Research Center, Tokyo University of Science, Noda, Chiba, Japan.
作者:
主题词
动物(Animals);脑(Brain);细胞系(Cell Line);疾病模型, 动物(Disease Models, Animal);果蝇属(Drosophila);果蝇蛋白质类(Drosophila Proteins);女(雌)性(Female);男(雄)性(Male);膜蛋白质类(Membrane Proteins);显微镜检查, 电子(Microscopy, Electron);运动活动(Motor Activity);突变(Mutation);过氧化物酶体类(Peroxisomes);Zellweger综合征(Zellweger Syndrome)
DOI
10.1371/journal.pone.0022984
PMID
21826223
发布时间
2021-10-20
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