第一作者:
Kim A,Staats
第一单位:
Laboratory of Neurobiology, Belgium; Leuven Research Institute of Neuroscience and Disease (LIND), KU Leuven, Belgium; Vesalius Research Center, VIB, Belgium. Electronic address: kim.staats@vib-kuleuven.be.
作者:
关键词
ALSAMPAAmyotrophic lateral sclerosisC9orf72DPP6ELP3ERExcitotoxicityFUS/TLSGFAPIP(3)ITPR2Motor neuron diseaseNeurogeneticsNuclear shrinkagePBSPCRPFN1PLCD1POAGPhospholipase C delta 1SDS-PAGESNPSOD1SOD1-G93A miceTAR-DNA binding protein 43TARDBPUBQLN2UNC13aamyotrophic lateral sclerosischromosome 9 open reading frame 72dipeptidyl-peptidase 6elongator protein 3endoplasmic reticulumfused in sarcoma/translocated in liposarcomaglial fibrillary acidic proteininositol 1,4,5-trisphosphateinositol 1,4,5-trisphosphate receptor 2phosphate buffered salinephosphoinositide phospholipase Cpolymerase chain reactionprimary open-angle glaucomaprofilin 1single nucleotide polymorphismsodium dodecyl sulfate polyacrylamide gel electrophoresissuperoxide dismutase 1ubiquilin 2unc-13 homolog Aα-amino-3-hydroxy-5-methyl-4-isoxazolepropionic acid
医学主题词
肌萎缩侧索硬化(Amyotrophic Lateral Sclerosis);动物(Animals);疾病模型, 动物(Disease Models, Animal);人类(Humans);小鼠(Mice);小鼠, 近交C57BL(Mice, Inbred C57BL);小鼠, 基因敲除(Mice, Knockout);小鼠, 转基因(Mice, Transgenic);神经元(Neurons);磷脂酶Cδ(Phospholipase C delta);脊髓(Spinal Cord);超氧化物歧化酶(Superoxide Dismutase);存活率分析(Survival Analysis)
DOI
10.1016/j.nbd.2013.08.006
PMID
23969236
发布时间
2016-11-25
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