第一作者:
Daniela,De Stefano
第一单位:
a European Institute for Research in Cystic Fibrosis; Division of Genetics and Cell Biology; San Raffaele Scientific Institute ; Milan , Italy.
作者:
关键词
BECN1/Beclin 1, autophagy-relatedCF, cystic fibrosisCFTRCFTR, cystic fibrosis transmembrane conductance regulatorCHX, cycloheximideCSNK2, casein kinase 2CXCL2, chemokine (C-X-C motif) ligand 2CXCL8, chemokine (C-X-C motif) ligand 8EGCG, epigallocatechin gallateFEV, forced expiratory volumePM, plasma membraneRPD, rectal potential differenceSQSTM1, sequestosome 1TGM2, transglutaminase 2TNF, tumor necrosis factorautophagycysteaminecystic fibrosisepigallocatechin gallatesweat chloride
主题词
衔接蛋白质类, 信号转导(Adaptor Proteins, Signal Transducing);投药, 口服(Administration, Oral);青少年(Adolescent);成年人(Adult);动物(Animals);凋亡调节蛋白质类(Apoptosis Regulatory Proteins);儿茶素(Catechin);细胞膜(Cell Membrane);儿童(Child);氯化物(Chlorides);胱胺(Cystamine);半胱胺(Cysteamine);囊性纤维化(Cystic Fibrosis);囊性纤维化跨膜传导调节因子(Cystic Fibrosis Transmembrane Conductance Regulator);女(雌)性(Female);纯合子(Homozygote);人类(Humans);白细胞介素8(Interleukin-8);男(雄)性(Male);膜蛋白质类(Membrane Proteins);小鼠(Mice);小鼠, 近交CFTR(Mice, Inbred CFTR);小鼠, 转基因(Mice, Transgenic);突变(Mutation);表型(Phenotype);试点项目(Pilot Projects);肿瘤坏死因子α(Tumor Necrosis Factor-alpha);青年人(Young Adult)
DOI
10.4161/15548627.2014.973737
PMID
25350163
发布时间
2022-03-09
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Autophagy
2053-74页
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