首页> American journal of respiratory cell and molecular biology> Deficiency Mutations of Alpha-1 Antitrypsin. Effects on Folding, Function, and Polymerization.

Deficiency Mutations of Alpha-1 Antitrypsin. Effects on Folding, Function, and Polymerization.

导出 OA

翻译打印收藏纠错

第一作者： Imran,Haq

第一单位： 1 Wolfson Institute for Biomedical Research, University College London, London, United Kingdom.;2 Institute of Structural and Molecular Biology/Birkbeck, University of London, London, United Kingdom.

作者： Imran,Haq ^[1] ; James A,Irving ^[1] ; Aarash D,Saleh ^[2] ; Louis,Dron ^[2] ; Gemma L,Regan-Mochrie ^[3] ; Neda,Motamedi-Shad ^[1] ; John R,Hurst ^[2] ; Bibek,Gooptu ^[4] ; David A,Lomas ^[5]

作者单位： 1 Wolfson Institute for Biomedical Research, University College London, London, United Kingdom.;2 Institute of Structural and Molecular Biology/Birkbeck, University of London, London, United Kingdom. ^[1] 3 London Alpha-1 Antitrypsin Deficiency Service, Royal Free Hospital, Pond Street, London, United Kingdom; and. ^[2] 1 Wolfson Institute for Biomedical Research, University College London, London, United Kingdom. ^[3] 2 Institute of Structural and Molecular Biology/Birkbeck, University of London, London, United Kingdom.;3 London Alpha-1 Antitrypsin Deficiency Service, Royal Free Hospital, Pond Street, London, United Kingdom; and.;4 Division of Asthma, Allergy and Lung Biology, King's College London, London, United Kingdom. ^[4] 1 Wolfson Institute for Biomedical Research, University College London, London, United Kingdom.;2 Institute of Structural and Molecular Biology/Birkbeck, University of London, London, United Kingdom.;3 London Alpha-1 Antitrypsin Deficiency Service, Royal Free Hospital, Pond Street, London, United Kingdom; and. ^[5]

关键词 alpha-1 antitrypsin deficiency mutation polymerization serpinopathies unfolding