第一作者:
Paola,Rusmini
第一单位:
Dipartimento di Scienze Farmacologiche e Biomolecolari (DiSFeB), Centro di Eccellenza sulle Malattie Neurodegenerative, Università degli Studi di Milano, Via Balzaretti 9, 20133, Milan, Italy.;Centro InterUniversitario sulle Malattie Neurodegenerative, Università degli Studi di Firenze, Genova, Roma Tor Vergata, Milan, Italy.
作者:
关键词
AggregationAndrogen receptorAutophagyBAG3CAG triplet repeatChaperonesERADHSPB8Misfolded proteinMotoneuron diseasesMuscleNeurodegenerationPolyglutamineProteasomeProtein quality control systemProteotoxicityRusmini Paola, Crippa Valeria, Greensmith Linda, and Poletti Angelo equally contributed to this study.SBMATestosteroneUPR
医学主题词
动物(Animals);延髓-脊髓肌萎缩症, X连锁(Bulbo-Spinal Atrophy, X-Linked);人类(Humans);肽类(Peptides);受体, 雄激素(Receptors, Androgen);三核苷酸重复扩增(Trinucleotide Repeat Expansion);非折叠蛋白质应答(Unfolded Protein Response)
DOI
10.1007/s12031-015-0675-6
PMID
26572535
发布时间
2018-11-13
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