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Human ALPI deficiency causes inflammatory bowel disease and highlights a key mechanism of gut homeostasis.

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作者单位: INSERM, UMR1163, Laboratory of Intestinal Immunity and Institut Imagine, Paris, France.;GENIUS group from ESPGHAN. [1] INSERM, UMR1163, Laboratory of Intestinal Immunity and Institut Imagine, Paris, France.;GENIUS group from ESPGHAN.;Université Paris Descartes-Sorbonne Paris Cité, Paris, France.;Department of Pediatric Gastroenterology, Assistance Publique-Hôpitaux de Paris Hôpital Necker-Enfants Malades, Paris, France. [2] SickKids Inflammatory Bowel Disease Center and Cell Biology Program, Research Institute, Hospital for Sick Children, Toronto, ON, Canada. [3] GENIUS group from ESPGHAN.;Unit of Pediatrics, Department of Human Pathology in Adulthood and Childhood "G. Barresi", University of Messina, Messina, Italy. [4] INSERM, UMR1163, Laboratory of Intestinal Immunity and Institut Imagine, Paris, France.;GENIUS group from ESPGHAN.;Université Paris Descartes-Sorbonne Paris Cité, Paris, France. [5] Department of Biochemistry, Biophysics and Structural Biology, Institute for Integrative Biology of the Cell (I2BC), CEA, UMR 9198 CNRS, Université Paris-Sud, Gif-sur-Yvette, France. [6] Digestive Endoscopy and Surgery Unit and Pathology Unit Bambino Gesù Children Hospital, IRCCS, Rome, Italy. [7] Université Paris Descartes-Sorbonne Paris Cité, Paris, France.;Department of Pathology, Necker-Enfants Malades Hospital Assistance Publique-Hôpitaux de Paris, Paris, France. [8] Bioinformatics Platform, Université Paris-Descartes-Paris Sorbonne Centre and Institut Imagine, Paris, France. [9] Genomic Platform, INSERM, UMR1163, Imagine Institute, Paris Descartes-Sorbonne Paris Cite University, Paris, France. [10] INSERM, UMR1163, Laboratory of Intestinal Immunity and Institut Imagine, Paris, France.;Université Paris Descartes-Sorbonne Paris Cité, Paris, France. [11] Department of Functional Coprology, Pitié Salpêtrière Hospital Assistance publique-Hôpitaux de Paris (AP-HP), Paris, France. [12] SickKids Inflammatory Bowel Disease Center and Cell Biology Program, Research Institute, Hospital for Sick Children, Toronto, ON, Canada aleixo.muise@sickkids.ca nadine.cerf-bensussan@inserm.fr.;Division of Gastroenterology, Hepatology, and Nutrition, Department of Pediatrics, Hospital for Sick Children, University of Toronto, Toronto, ON, Canada.;Department of Biochemistry, Institute of Medical Science, University of Toronto, Toronto, ON, Canada. [13] INSERM, UMR1163, Laboratory of Intestinal Immunity and Institut Imagine, Paris, France aleixo.muise@sickkids.ca nadine.cerf-bensussan@inserm.fr.;GENIUS group from ESPGHAN.;Université Paris Descartes-Sorbonne Paris Cité, Paris, France. [14]
DOI 10.15252/emmm.201708483
PMID 29567797
发布时间 2024-12-13
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