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Elevated TGF β2 serum levels in Emery-Dreifuss Muscular Dystrophy: Implications for myocyte and tenocyte differentiation and fibrogenic processes.

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第一作者: Pia,Bernasconi
第一单位: a Neurology IV - Neuroimmunology and Neuromuscular Diseases Unit , Foundation IRCCS Neurological Institute "Carlo Besta" , Milan , Italy.
作者单位: a Neurology IV - Neuroimmunology and Neuromuscular Diseases Unit , Foundation IRCCS Neurological Institute "Carlo Besta" , Milan , Italy. [1] b Neurology Department , Hospital San Francesco of Nuoro , Nuoro , Italy. [2] c Department of Clinical and Experimental Medicine , University of Pisa , Pisa , Italy. [3] d Cardiomyology and Medical Genetics, Department of Experimental Medicine , Campania University "Luigi Vanvitelli" (former denomination: Second University of Naples) , Italy. [4] e Department of Neurosciences "Rita Levi Montalcini" , University of Turin , Turin , Italy. [5] f Institute of Applied Sciences and Intelligent Systems "ISASI Edoardo Caianello", National Research Council of Italy , Messina , Italy. [6] g Istituto di Cardiologia, Università di Bologna, Policlinico S.Orsola-Malpighi , Bologna , Italy. [7] h Cardiology Division, Department of Diagnostics , Clinical and Public Health Medicine, University of Modena and Reggio Emilia, Policlinico di Modena , Modena , Italy. [8] i Department of Neurosciences , Odontostomatological and Reproductive Sciences, University of Naples "Federico II" , Naples , Italy. [9] j Institute of Molecular Genetics (IGM)-CNR, Unit of Bologna , Bologna , Italy.;k Laboratory of Musculoskeletal Cell Biology , Rizzoli Orthopaedic Institute , Bologna , Italy. [10] l Department of Neurosciences , Neuromuscular Center, University of Padova , Padova , Italy. [11] k Laboratory of Musculoskeletal Cell Biology , Rizzoli Orthopaedic Institute , Bologna , Italy. [12] m Istituto Nazionale di Genetica Molecolare "Romeo and Enrica Invernizzi" , Milan , Italy.;n Institute of Cell Biology and Neurobiology, IRCCS Santa Lucia Foundation , Rome , Italy. [13] o Sorbonne Universités , UPMC Univ Paris 06, INSERM UMRS974, CNRS FRE3617, Center for Research in Myology, Institut de Myologie, G.H. Pitié Salpêtrière , Paris Cedex 13, France. [14]
DOI 10.1080/19491034.2018.1467722
PMID 29693488
发布时间 2019-09-19
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