第一单位:
Clinical Research Unit, Avicenne University Hospital, AP-HP, Bobigny, France; Paris 13 University, Sorbonne Paris Cité, Paris, France; Laboratory of Cellular and Molecular Mechanisms of Hematological Disorders and Therapeutical Implications, INSERM UMR1163/CNRS URL 8254, Paris, France; French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France. Electronic address: coralie.bloch-queyrat@aphp.fr.
作者:
Coralie,Bloch [1]
;
Jean Philippe,Jais [2]
;
Marine,Gil [3]
;
Marouane,Boubaya [4]
;
Yves,Lepelletier [5]
;
Brigitte,Bader-Meunier [6]
;
Nizar,Mahlaoui [7]
;
Nicolas,Garcelon [3]
;
Olivier,Lambotte [8]
;
David,Launay [9]
;
Claire,Larroche [10]
;
Estibaliz,Lazaro [11]
;
Francois,Liffermann [12]
;
Olivier,Lortholary [13]
;
Marc,Michel [14]
;
Jean-Marie,Michot [15]
;
Pierre,Morel [16]
;
Morgane,Cheminant [17]
;
Felipe,Suarez [17]
;
Louis,Terriou [9]
;
Geoffrey,Urbanski [18]
;
Jean-Francois,Viallard [19]
;
Alexandre,Alcais [2]
;
Alain,Fischer [20]
;
Geneviève,de Saint Basile [21]
;
Olivier,Hermine [22]
;
French HLH Study Group
作者单位:
Clinical Research Unit, Avicenne University Hospital, AP-HP, Bobigny, France; Paris 13 University, Sorbonne Paris Cité, Paris, France; Laboratory of Cellular and Molecular Mechanisms of Hematological Disorders and Therapeutical Implications, INSERM UMR1163/CNRS URL 8254, Paris, France; French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France. Electronic address: coralie.bloch-queyrat@aphp.fr.
[1]
Imagine Institute, Université Paris Cité, Paris, France; Biostatistic Unit, Necker University Hospital, AP-HP, Paris, France; Human Genetics of Infectious Diseases: Complex Predisposition, INSERM UMR1163, Paris, France.
[2]
Imagine Institute, Université Paris Cité, Paris, France.
[3]
Clinical Research Unit, Avicenne University Hospital, AP-HP, Bobigny, France.
[4]
Laboratory of Cellular and Molecular Mechanisms of Hematological Disorders and Therapeutical Implications, INSERM UMR1163/CNRS URL 8254, Paris, France; Imagine Institute, Université Paris Cité, Paris, France.
[5]
Imagine Institute, Université Paris Cité, Paris, France; Department of Pediatric Immunology and Rheumatology, Necker University Hospital, AP-HP, Paris, France.
[6]
French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France; Department of Pediatric Immunology and Rheumatology, Necker University Hospital, AP-HP, Paris, France.
[7]
University Paris Saclay, AP-HP, Hôpital Bicêtre, IMVAHB UMR1184, INSERM, CEA, Le Kremlin Bicêtre, France.
[8]
Université de Lille, CHU Lille, Département de Médecine Interne et Immunologie Clinique, Centre de Référence des Maladies Auto-immunes Systémiques Rares du Nord et Nord-Ouest de France, Lille, France; INSERM INFINITE U1286, Lille, France.
[9]
Internal Medicine Unit, Avicenne Hospital, AP-HP, Bobigny, France.
[10]
Internal Medicine Department, Bordeaux Hospital University, Bordeaux, France; CNRS-UMR 5164 Immuno ConcEpT, Bordeaux, France.
[11]
Service de medecine interne-hematologie, Centre hospitalier de Dax, Dax, France.
[12]
French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France; Service de Maladies Infectieuses et Tropicales, Centre d'Infectiologie Necker Pasteur, Hôpital Universitaire Necker-Enfants Malades, Assistance Publique-Hôpitaux de Paris, Université de Paris, Paris, France.
[13]
Department of Internal Medicine, Centre de Référence maladies rares sur les Cytopénies Auto-Immunes de l'adulte, Hôpitaux Universitaires Henri Mondor, AP-HP, Université Paris-Est Créteil, Créteil, France.
[14]
Gustave Roussy, University Paris Saclay, Drug Development Department, Villejuif, France.
[15]
Service d'Hématologie Clinique, Hôpital Schaffner de Lens, Lens Cedex, France.
[16]
Laboratory of Cellular and Molecular Mechanisms of Hematological Disorders and Therapeutical Implications, INSERM UMR1163/CNRS URL 8254, Paris, France; French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France; Clinical Hematology, Necker University Hospital, AP-HP, Paris, France.
[17]
Department of Internal Medicine and Clinical Immunology, University Hospital, Angers, France; MitoLab Team, MITOVASC Institute, UMR CNRS 6015, INSERM U1083, University of Angers, Angers, France.
[18]
Internal Medicine Department, Bordeaux Hospital University, Bordeaux, France.
[19]
French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France; Department of Pediatric Immunology and Rheumatology, Necker University Hospital, AP-HP, Paris, France; Laboratory of Normal and Pathological Homeostasis of the Immune System, INSERM UMR1163, Paris, France; Necker University Hospital, AP-HP, Paris, France; College de France, Paris, France.
[20]
French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France; Laboratory of Normal and Pathological Homeostasis of the Immune System, INSERM UMR1163, Paris, France.
[21]
Laboratory of Cellular and Molecular Mechanisms of Hematological Disorders and Therapeutical Implications, INSERM UMR1163/CNRS URL 8254, Paris, France; French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France; Clinical Hematology, Necker University Hospital, AP-HP, Paris, France. Electronic address: ohermine@gmail.com.
[22]
DOI
10.1016/j.jaci.2023.07.023
PMID
37678575
发布时间
2024-02-16