Niemann-Pick C1 protein: obligatory roles for N-terminal domains and lysosomal targeting in cholesterol mobilization.
第一作者:
H,Watari
第一单位:
Center for Research on Reproduction and Women's Health, Departments of Obstetrics and Gynecology, University of Pennsylvania Medical Center, Philadelphia, PA 19104, USA.
作者:
医学主题词
氨基酸取代(Amino Acid Substitution);动物(Animals);CHO细胞(CHO Cells);载体蛋白质类(Carrier Proteins);胆固醇(Cholesterol);仓鼠亚科(Cricetinae);内质网(Endoplasmic Reticulum);非律平(Filipin);绿色荧光蛋白质类(Green Fluorescent Proteins);人类(Humans);细胞内信号肽和蛋白质类(Intracellular Signaling Peptides and Proteins);发光蛋白质类(Luminescent Proteins);溶酶体(Lysosomes);膜糖蛋白类(Membrane Glycoproteins);诱变, 定点(Mutagenesis, Site-Directed);尼曼-皮克病(Niemann-Pick Diseases);蛋白质类(Proteins);重组蛋白质类(Recombinant Proteins);序列缺失(Sequence Deletion);转染(Transfection)
DOI
10.1073/pnas.96.3.805
PMID
9927649
发布时间
2024-09-22
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