摘要喉软骨发育不良又称先天性喉软骨软化症或先天性喉喘鸣,是临床比较常见的婴幼儿喉部疾病,常表现为由于喉或气管发生阻塞,患者用力呼吸时,气流通过喉或气管狭窄处发出特殊声音,即喉喘鸣。阻塞的原因可以是气道管腔内,也可以是外压性。气道阻塞部位可位于鼻、咽、喉及气管。临床上多种疾病可引起喉喘鸣,如先天性喉喘鸣、急性喉炎或急性喉气管支气管炎、呼吸道异物、先天性喉狭窄及喉蹼等。该文就喉软骨发育不良的病因、病理、临床表现、诊断及治疗等进行综述。
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abstractsLaryngeal cartilage dysplasia,also known as congenital laryngeal cartilage softening or con-genital laryngeal stridor,a clinical common laryngeal disease in infant. It is often shown as airflow makes special sound through larynx or tracheal stenosis,also known as laryngeal stridor. Obstruction can be caused by airway lumen or external pressure. Airway obstruction position can be located in the nose,pharynx and larynx and tra-chea. Laryngeal stridor can be caused by many diseases,such as congenital laryngeal stridor,acute laryngeal,or acute laryngotracheobronchitis,respiratory tract foreign bodies,congenital laryngeal stenosis and laryngeal web, etc. The pathogenesis,pathology,clinical manifestation,diagnosis and treatment are reviewed.
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