摘要目的 通过我院1例左心发育不全综合征治疗的成功案列,探讨左心发育不全综合征的外科治疗.方法 检索国内外外科治疗左心发育不全综合征的相关文献,结合我院病例,阐述国内左心发育不全综合征治疗现状,对左心发育不全综合征的外科治疗进行详细总结.结果 我院1例左心发育不全综合征患儿在行Norwood Ⅰ期+Sano术后顺利恢复出院.临床经验及文献检索都表明我国仅少数医院成功实施了Norwood手术,术后维持体-肺循环的动态平衡是患儿存活的关键.结论 我国对左心发育不全综合征的外科治疗仍处于起步阶段,Norwood手术是治疗左心发育不全综合征的有效方法,维持体-肺循环的动态平衡是患儿存活的关键.

abstractsObjective To summarize the surgical experience of hypoplastic left heart syndrome (HLHS).Methods Based on clinical profiles and databases,current domestic status was discussed for surgical treatment of HLHS.Results One child with HLHS was successfully operated at our hospital.Clinical experiences and literature searches shown that only few domestic hospitals had successfully implemented Norwood surgery.Postoperative maintenance of body-pulmonary vascular balance is essential for survival.Conclusions Surgical treatment of HLHS is still elementary in China.Norwood surgery is an effective treatment for HLHS and maintaining a dynamic balance of bodypulmonary circulation is vital.