摘要目的 探讨产前超声对胎儿心室双出口的诊断价值.方法 收集2010 －2018年期间,中南大学湘雅二医院、常德市妇幼保健院产前超声诊断中心诊断为心室双出口胎儿的超声检查资料,将其超声特征与产后超声心动图、手术和尸体解剖结果进行对照分析.结果 产前超声共诊断94例心室双出口,其中右心室双出口84例,左心室双出口10例.尸体解剖45例,其中42例证实为心室双出口, 1例法洛四联症, 2例完全型大动脉转位; 49例继续妊娠,其中手术证实32例,产后超声心动图证实17例.心室双出口的主要特征为两根大血管全部或大部分(＞50%)起源于同一心室.结论 心室双出口的产前超声诊断具有重要的临床价值,便于产前咨询和产后处理,应与大动脉转位、法洛四联症和室间隔缺损鉴别.

abstractsObjective To investigate the clinical value of prenatal diagnosis of fetal double outlet ventricle . Methods T he data of double outlet ventricle from fetal echocardiography in Second Xiangya Hospital of Central South University and Changde Women and Children Health Hospital of Hunan Province from January 2000 to August 2018 were collected . T he statistical method was used to analyze characteristics of echocardiography ,related‐intracardiac and extracardiac abnormalities ,postnatal echocardiography ,surgery and autopsy findings . Results Ninety‐four fetuses were diagnosed with double outlet ventricle ,including 84 cases of double outlet right ventricle ( DORV ) and 10 cases of double outlet left ventricle ( DOLV ) . T he pregnancy was terminated in 45 cases . Autopsy was offered to all patients after termination of pregnancy ,42 cases were consistent with prenatal diagnosis ,1 case was tetralogy of fallot ,2 cases were transposition of great artery . Forty‐nine cases were decided to continue the pregnancy ,32 cases of them were confirmed by postpartum surgery ,17 cases were confirmed by postnatal echocardiography . Echocardiographic findings of fetal double outlet ventricle was characterized by the origin of the both great arteries arising predominantly or completely( ＞50% ) from the same ventricle . Conclusions Prenatal ultrasound diagnosis of double outlet ventricular has important clinical value ,facilitate appropriate prenatal counseling and postnatal management and it should be differentiated with transposition of the great arteries ,tetralogy of fallot and ventricular septal defect .