摘要Objective:This study aimed to investigate the long-term auditory and speech outcomes of sequential bilateral cochlear implantation(BiCI)in children with cochlear nerve deficiency(CND).Methods:Sixteen CND children who underwent sequential BiCI were retrospectively reviewed.Auditory and speech abilities were evaluated using questionnaire-based rating scales,including the Categories of Auditory Performance(CAP),the Infant-Toddler Meaningful Auditory Integration Scale(IT-MAIS),and the Speech Intelligibility Rating(SIR).Closed-set and open-set speech recognition abilities were also measured.Results:The first cochlear implantation(CI)was performed at a median age of 12 months.The mean age at contralateral CI was 43 months,and the mean inter-implant interval time was 26 months.All patients showed continuous auditory and speech improvement over time.Of the sixteen patients,nine completed closed-set and/or open-set speech recognition assessments.After contralateral CI,all nine patients showed improved closed-set speech recognition scores.Four patients achieved closed-set test scores of more than 90％and open-set disyllable recognition scores ranging from 44 to 85％.In addition,two patients demonstrated better performance with bilateral CI than with unilateral CI.Conclusions:CND children showed favorable long-term auditory and speech outcomes after sequential BiCI,and some demonstrated bilateral benefit in speech perception.These findings suggest that BiCI may be a viable option for selected CND children.