摘要上皮样血管内皮瘤是一类发病率低的低度恶性肿瘤,肿瘤位于肝脏称为肝上皮样血管内皮瘤(HEHE),可发生转移及术后复发.由于疾病的罕见性,国内外文献报道的病例较少,治疗方法也存在争议.随着肝移植手术的发展,肝移植越来越多应用于治疗因HEHE导致肝功能衰竭的患者.本文回顾HEHE的疾病特点,肝移植治疗HEHE的适应证、免疫治疗以及预后等,简述肝移植治疗HEHE的现状与进展.

abstractsEpithelioid Hemangioendotheliomais a rare, low-grade malignant vascular tumour. It' scalled hepatic epithelioid hemangioendothelioma( HEHE) , when it occurs in liver. It can be metastatic and postoperative recurrence. There are few cases have been reported in the literature at home and abroad because of its rarity. The treatment of HEHE is also controversial. With the continuous improvement of surgical techniques of liver transplantation, it is increasingly applied to treat liver failure patients caused by HEHE. Our paper reviews the literature on disease characteristics of HEHE, and liver transplantation for HEHE indications, immunotherapy and prognosis, to illustrate the status and progress of liver transplantation for HEHE.