摘要目的 分析并探讨横纹肌样脑膜瘤的临床诊疗特点及预后. 方法 回顾性分析广州医学院第二附属医院神经外科收治的2例横纹肌样脑膜瘤患者的临床资料,并复习相关文献报道. 结果 2例患者均行肉眼全切除(Simpson Ⅰ级),术后未行放化疗,随访期限分别为2年和2个月.第1例于术后第2年复发,因未行再次手术而死亡.另1例术后2月因颅内感染死于全身并发症. 结论 横纹肌样脑膜瘤术前诊断困难,手术为治疗的首选,术后常于短期内复发,患者预后不佳.

abstractsObjective To analyze the clinical diagnosis,treatment and prognosis of rhabdoid meningioma.Methods Two cases of rhabdoid meningioma treated in our department were analyzed retrospectively,and the relevant literatures were reviewed.Results Both of the two patients underwent complete meningioma removal under microscope(Simpson grade I)without postoperative radiotherapy or chemotherapy.The two patients were followed up for 2 months and 2 years.One patient experienced meningioma recurred 2 years after the operative,and died due to refusal of a second operation.The other patient died of systemic complications secondary to postoperative intracranial infection.Conclusion The preoperative diagnosis of rhabdoid meningioma can be difficult,and surgical meningioma removal remains the primary choice of treatment.The patients often experience meningioma recurrence shortly after the operation with poor prognosis.Early postoperative radiochemotherapy may prove beneficial in prolonging the survival of patients.