摘要目的 探讨Kelly手术治疗膀胱外翻-尿道上裂复合畸形的短期疗效.方法 回顾性分析2015年12月以来我院5例采用Kelly手术治疗的男性膀胱外翻-尿道上裂复合畸形患儿的临床资料.年龄14个月~3岁4个月,中位年龄14个月.内容包括患儿的基本情况、术前诊断、手术方法;并进行随访,内容包括术后恢复、排尿控制、阴茎外观和并发症等.结果 5例患儿中膀胱外翻2例,均已进行第一期膀胱和腹壁关闭,但尿道上裂和尿控未处理;另3例为阴茎耻骨部尿道上裂,2例伴压力性尿失禁,1例为完全性尿失禁.5例患儿均接受Kelly手术,包括肛提肌游离重建尿道括约肌、改良Young-Dees-Leadbetter方法膀胱颈部重建、改良Cantwell-Ransley方法尿道上裂修复等.术后随访2~12个月,平均7.8个月.5例患儿均获得功能性控尿,4例排尿控制Ⅰ级,1例术前完全性尿失禁的患儿排尿控制Ⅱ级;5例患儿均排尿通畅,无残余尿.4例阴茎外观明显改善,全部病例未出现伤口裂开、伤口感染、阴茎头坏死、阴茎体坏死、尿道狭窄、尿瘘等并发症.结论 Kelly手术在术后短期内能有效改善膀胱外翻-尿道上裂复合畸形患儿的尿控,并延长大多数病例的阴茎长度,获得满意的阴茎外观.但手术操作复杂,术中暴露、保护阴部内血管和神经束是避免阴茎血供受影响的关键.

abstractsObjective To evaluate the short-term outcome of the Kelly procedure for bladder exstrophy-epispadias complex.Methods Kelly procedure was performed in 5 cases from December 2015 in our institute. Retrospective analysis was done including the surgery and follow up.Results Two bladder exstrophy boys had histories of primary bladder closure without bladder neck reconstruction during the neonatal period. Another three epispadias boys had sever urethral defects with full incontinence. All cases undertook Kelly procedure and were followed up for 7.8 months (2-12 months). No severe complications such as glanular necrosis, urethral stricture and urethrocutaneous fistula was observed. Four cases were fully continent and one epispadias case had stress incontinence.Conclusions Kelly procedure produced satisfactory urinary continence and phallic cosmetics in bladder exstrophy-epispadias complex in children. Proper identification of the pudendal neurovascular bundle and repair of the external sphincter by levatorplasty help improve the outcome.